Peripheral T-Cell Lymphoma

A heterogeneous group of aggressive non-Hodgkin lymphomas derived from mature T cells. Includes PTCL-NOS, angioimmunoblastic T-cell lymphoma, and ALK-negative anaplastic large cell lymphoma. Generally poor prognosis with standard chemotherapy.

Quick Answer

What it is

A heterogeneous group of aggressive non-Hodgkin lymphomas derived from mature T cells. Includes PTCL-NOS, angioimmunoblastic T-cell lymphoma, and ALK-negative anaplastic large cell lymphoma.

Key findings

  • Grade A: Overall Response Rate (PTCL) (Romidepsin (Istodax))
  • Grade A: Duration of Response (PTCL) (Romidepsin (Istodax))
  • Grade B: Response by Prior Therapy (Romidepsin (Istodax))

Safety

No specific caution or interaction language was detected in the current summary/outcome notes.

ℹ️ Quick Facts

Quick Facts: Peripheral T-Cell Lymphoma

  • Supplements Studied:1
1 supps · 3 outcomes

Detailed Outcomes

A
Overall Response Rate (PTCL)
Pivotal Phase 2 trial (n=130): ORR 25% with 15% CR/CRu. NCI multicenter study (n=47): ORR 38% with 17% CR. Responses seen across all major PTCL subtypes. Led to FDA approval June 2011.
moderateImproves
A
Duration of Response (PTCL)
Pivotal trial: Median DOR 28 months in responders. NCI trial: Median DOR 8.9 months (range 2-74 months). Durable responses possible in heavily pretreated patients (median 3 prior therapies).
largeImproves
B
Response by Prior Therapy
Responses observed regardless of number or type of prior therapies. Patients with up to 11 prior treatments responded. 38% of patients had prior stem cell transplant and still achieved responses.
moderateImproves

Research Citations (47)

The HDAC inhibitor romidepsin renders liver cancer vulnerable to RTK targeting and immunologically active.
(2025)
PMID: 40855049
Acetylation-dependent regulation of core spliceosome modulates hepatocellular carcinoma cassette exons and sensitivity to PARP inhibitors.
(2024)
PMID: 38890388
Oral azacitidine compared with standard therapy in patients with relapsed or refractory follicular helper T-cell lymphoma (ORACLE): an open-label randomised, phase 3 study.
(2024)
PMID: 38796193
Duvelisib plus romidepsin in relapsed/refractory T cell lymphomas: a phase 1b/2a trial.
(2024)
PMID: 38886623
Multicenter phase 2 study of romidepsin plus lenalidomide for previously untreated peripheral T-cell lymphoma.
(2023)
PMID: 37327113
Romidepsin (FK228) improves the survival of allogeneic skin grafts through downregulating the production of donor-specific antibody via suppressing the IRE1α-XBP1 pathway.
(2022)
PMID: 35557040
Organ-specific toxicity of romidepsin in patients with preexisting cardiovascular disease: a retrospective analysis.
(2022)
PMID: 35272538
Romidepsin Treatment in Patients With Relapsed or Refractory Peripheral T-Cell Lymphoma: A Systematic Review and Meta-Analysis.
(2022)
PMID: 34264886
Effect of 3BNC117 and romidepsin on the HIV-1 reservoir in people taking suppressive antiretroviral therapy (ROADMAP): a randomised, open-label, phase 2A trial.
(2022)
PMID: 35544074
Early intervention with 3BNC117 and romidepsin at antiretroviral treatment initiation in people with HIV-1: a phase 1b/2a, randomized trial.
(2022)
PMID: 36253609

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