Cutaneous T-Cell Lymphoma

A group of rare non-Hodgkin lymphomas where malignant T lymphocytes accumulate in the skin. Includes mycosis fungoides and Sezary syndrome. Presents with skin patches, plaques, or tumors. Progressive disease can spread to lymph nodes and internal organs.

Quick Answer

What it is

A group of rare non-Hodgkin lymphomas where malignant T lymphocytes accumulate in the skin. Includes mycosis fungoides and Sezary syndrome.

Key findings

  • Grade A: Overall Response Rate (CTCL) (Romidepsin (Istodax))
  • Grade A: Pruritus Improvement (CTCL) (Romidepsin (Istodax))

Safety

No specific caution or interaction language was detected in the current summary/outcome notes.

ℹ️ Quick Facts

Quick Facts: Cutaneous T-Cell Lymphoma

  • Supplements Studied:1
1 supps · 2 outcomes

Detailed Outcomes

A
Overall Response Rate (CTCL)
Two pivotal Phase 2 trials in relapsed/refractory CTCL (n=71, n=96): ORR 34-35% with 6% CR in both studies. Among 68 patients with advanced disease, 38% achieved response including 5 CRs. Led to FDA approval Nov 2009.
moderateImproves
A
Pruritus Improvement (CTCL)
43% (28/65) of patients with moderate-severe pruritus at baseline achieved improvement. Important quality of life benefit in CTCL where pruritus is often debilitating.
moderateImproves

Research Citations (47)

The HDAC inhibitor romidepsin renders liver cancer vulnerable to RTK targeting and immunologically active.
(2025)
PMID: 40855049
Acetylation-dependent regulation of core spliceosome modulates hepatocellular carcinoma cassette exons and sensitivity to PARP inhibitors.
(2024)
PMID: 38890388
Oral azacitidine compared with standard therapy in patients with relapsed or refractory follicular helper T-cell lymphoma (ORACLE): an open-label randomised, phase 3 study.
(2024)
PMID: 38796193
Duvelisib plus romidepsin in relapsed/refractory T cell lymphomas: a phase 1b/2a trial.
(2024)
PMID: 38886623
Multicenter phase 2 study of romidepsin plus lenalidomide for previously untreated peripheral T-cell lymphoma.
(2023)
PMID: 37327113
Romidepsin (FK228) improves the survival of allogeneic skin grafts through downregulating the production of donor-specific antibody via suppressing the IRE1α-XBP1 pathway.
(2022)
PMID: 35557040
Organ-specific toxicity of romidepsin in patients with preexisting cardiovascular disease: a retrospective analysis.
(2022)
PMID: 35272538
Romidepsin Treatment in Patients With Relapsed or Refractory Peripheral T-Cell Lymphoma: A Systematic Review and Meta-Analysis.
(2022)
PMID: 34264886
Effect of 3BNC117 and romidepsin on the HIV-1 reservoir in people taking suppressive antiretroviral therapy (ROADMAP): a randomised, open-label, phase 2A trial.
(2022)
PMID: 35544074
Early intervention with 3BNC117 and romidepsin at antiretroviral treatment initiation in people with HIV-1: a phase 1b/2a, randomized trial.
(2022)
PMID: 36253609

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